Schnitzler syndrome: validation and applicability of diagnostic criteria in real-life patients.

Date publication

février 2017

Journal

Allergy

Auteurs

Membres identifiés du Cancéropôle Est :
Pr AUBIN François , Pr LIPSKER Dan , Pr SAULEAU Erik-André , Pr GOTTENBERG Jacques-Eric

Tous les auteurs :
Gusdorf L, Asli B, Barbarot S, Néel A, Masseau A, Puéchal X, Gottenberg JE, Grateau G, Blanchard-Delaunay C, Rizzi R, Lifermann F, Kyndt X, Aubin F, Bessis D, Boye T, Gayet S, Rongioletti F, Sauleau E, Fermand JP, Lipsker D

Lien Pubmed

https://www.ncbi.nlm.nih.gov/pubmed/27564982

Résumé

Schnitzler syndrome is characterized by an urticarial rash, a monoclonal gammopathy, and clinical, histological, and biological signs of neutrophil-mediated inflammation. The aim of this study was to assess the applicability and validity of the existing diagnostic criteria in real-life patients.

Mots clés

Schnitzler syndrome, auto-inflammatory disease, diagnostic criteria, monoclonal gammopathy, neutrophilic urticarial dermatosis

Référence

Allergy. 2017 Feb;72(2):177-182