Fiche publication
Date publication
mai 2018
Journal
Revue neurologique
Auteurs
Membres identifiés du Cancéropôle Est :
Dr DEVILLIERS Hervé
Tous les auteurs :
Brenière C, Blanc C, Devilliers H, Samson M, Delpont B, Bielefeld P, Besancenot JF, Giroud M, Béjot Y
Lien Pubmed
Résumé
Behçet's disease is a rare multisystemic vasculitis with an etiology that is still unknown. Neurological manifestations may be seen in approximately 5-15% of patients, and both parenchymal and extraparenchymal neurological involvement has been described. When cerebral venous thrombosis (CVT) is the main extraparenchymal manifestation of Behçet's disease, the condition is then dubbed "angio-Behçet's syndrome". However, arterial involvement is extremely rare, with only one reported case of vasculo-neuro-Behçet's disease, characterized by both venous and intracranial arterial involvement - until now. This report is of two patients diagnosed with Behçet's disease characterized by the concomitant presence of both cerebral arterial manifestations and CVT.
Mots clés
Arterial aneurysm, Behçet's disease, Cerebral venous thrombosis, Ischemic stroke, Vasculo-Behçet's disease
Référence
Rev. Neurol. (Paris). 2018 May;174(5):337-341
