Fiche publication


Date publication

septembre 2016

Journal

Pediatric blood & cancer

Auteurs

Membres identifiés du Cancéropôle Est :
Pr AUBER Frédéric


Tous les auteurs :
Scalabre A, Bergeron C, Brioude F, Dainese L, Cropet C, Coulomb L'hermine A, Pasqualini C, Auber F, Verschuur A, Schleiermacher G, Le Bouc Y, Audry G, Irtan S

Résumé

Patients with Beckwith-Wiedemann syndrome (BWS) or isolated hemihypertrophy (HH) treated for a Wilms tumor (WT) carry an increased risk of developing metachronous lesion. There are no guidelines on precise indications for nephron sparing surgery (NSS) in unilateral WT (UWT). The objective of this retrospective study was to delineate the indications of NSS in patients with BWS/HH treated for WT and to evaluate their outcome.

Mots clés

Beckwith-Wiedemann Syndrome, surgery, Child, Child, Preschool, Female, Humans, Hyperplasia, surgery, Infant, Kidney Neoplasms, surgery, Male, Nephrons, surgery, Retrospective Studies, Wilms Tumor, surgery

Référence

Pediatr Blood Cancer. 2016 09;63(9):1571-7