Fiche publication
Date publication
juin 2015
Journal
Archives de pediatrie : organe officiel de la Societe francaise de pediatrie
Auteurs
Membres identifiés du Cancéropôle Est :
Pr CHASTAGNER Pascal
Tous les auteurs :
Hernandez M, Droz D, Mansuy L, Simon E, Chastagner P
Lien Pubmed
Résumé
Ewing sarcoma is the second most common primary malignant bone cancer in children and adolescents. Clinical presentation is usually dominated by local pain and a palpable mass. These symptoms justify imaging investigations: the first one, when an osseous lesion is suspected, is usually a conventional radiograph in two planes. Ewing sarcoma appears as a poorly defined osteolytic lesion that may frequently be associated with cortical erosion or laminar periosteal response ("onion skin"). However, this aspect is not pathognomonic and the definitive diagnosis is made by biopsy. Absence of pain or an unusual localization can lead to misdiagnosis. We report the case of a 7-year-old boy with Ewing sarcoma located in the mandible with a clinical picture including progressive mandibular swelling but no pain.
Mots clés
Child, Humans, Male, Mandibular Neoplasms, diagnosis, Sarcoma, Ewing, diagnosis
Référence
Arch Pediatr. 2015 Jun;22(6):626-9
