Fiche publication


Date publication

juillet 2022

Journal

Current opinion in pulmonary medicine

Auteurs

Membres identifiés du Cancéropôle Est :
Pr BONNIAUD Philippe


Tous les auteurs :
Cottin V, Si-Mohamed S, Diesler R, Bonniaud P, Valenzuela C

Résumé

Pleuroparenchymal fibroelastosis (PPFE) is a clinico-radiologic-pathologic interstitial lung disease (ILD) characterized by fibrosis that has upper lobe and subpleural predominance, involving both the visceral pleura and the subjacent subpleural lung parenchyma, and comprises dense fibroelastic changes with prominent elastosis of the alveolar walls together with fibrous thickening of the visceral pleura. The goal of this review is to summarize the state-of-the-art understanding in PPFE.

Référence

Curr Opin Pulm Med. 2022 07 19;: