Fiche publication
Date publication
janvier 2017
Journal
European journal of gynaecological oncology
Auteurs
Membres identifiés du Cancéropôle Est :
Pr NOEL Georges
,
Pr AKLADIOS Chérif
Tous les auteurs :
Koch A, Frigo S, Lecointre L, Hummel M, Akladios CY, Bergerat JP, Noël G, Wattiez A
Lien Pubmed
Résumé
Primitive Neuroectodermal tumor belongs to the family of Ewing's tumor and is characterized by at (11;22) (q24;ql2) or at (21;22) (q22;ql2) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no specific characteristics for imaging. The diagnosis is made on histological examination of the surgical spec- imen or biopsies. Radiotherapy and chemotherapy complete the treatment. The authors report the case of a 26-year-old patient who only had pelvic discomfort. Diagnostic laparoscopy showed a retroperitoneal and retrovesical mass of five centimeters. The patient benefited from adjuvant chemotherapy and radiotherapy. She is free of disease 30 months after treatment.
Mots clés
Adult, Chemotherapy, Adjuvant, Diagnostic Techniques, Surgical, Female, Humans, Laparoscopy, Neuroectodermal Tumors, Primitive, diagnosis, Positron-Emission Tomography, Radiotherapy, Adjuvant, Retroperitoneal Neoplasms, diagnosis
Référence
Eur J Gynaecol Oncol. 2017 ;38(2):314-318