Fiche publication


Date publication

janvier 2017

Journal

European journal of gynaecological oncology

Auteurs

Membres identifiés du Cancéropôle Est :
Pr NOEL Georges , Pr AKLADIOS Chérif


Tous les auteurs :
Koch A, Frigo S, Lecointre L, Hummel M, Akladios CY, Bergerat JP, Noël G, Wattiez A

Résumé

Primitive Neuroectodermal tumor belongs to the family of Ewing's tumor and is characterized by at (11;22) (q24;ql2) or at (21;22) (q22;ql2) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no specific characteristics for imaging. The diagnosis is made on histological examination of the surgical spec- imen or biopsies. Radiotherapy and chemotherapy complete the treatment. The authors report the case of a 26-year-old patient who only had pelvic discomfort. Diagnostic laparoscopy showed a retroperitoneal and retrovesical mass of five centimeters. The patient benefited from adjuvant chemotherapy and radiotherapy. She is free of disease 30 months after treatment.

Mots clés

Adult, Chemotherapy, Adjuvant, Diagnostic Techniques, Surgical, Female, Humans, Laparoscopy, Neuroectodermal Tumors, Primitive, diagnosis, Positron-Emission Tomography, Radiotherapy, Adjuvant, Retroperitoneal Neoplasms, diagnosis

Référence

Eur J Gynaecol Oncol. 2017 ;38(2):314-318