Moya-Moya syndrome after cranial radiation for optic glioma with NF1. Case report and literature review of syndromic cases.

Fiche publication


Date publication

mars 2018

Journal

Neuro-Chirurgie

Auteurs

Membres identifiés du Cancéropôle Est :
Pr MOULIN Thierry


Tous les auteurs :
Brandicourt P, Bonnet L, Béjot Y, Drouet C, Moulin T, Thines L

Résumé

Moya-Moya angiopathy is a neurovascular disease that predisposes to ischemic or hemorrhagic strokes. It is generated by a steno-occlusion of the terminal portion of the internal carotid arteries, which induces the development of abnormal neovessels in the deep regions of the brain. Some pathologies such as sickle cell disease, Down syndrome or Graves' disease may be associated with Moya-Moya angiopathy. These syndromic forms harbor several differences compared with idiopathic Moya-Moya disease.

Mots clés

Cranial irradiation, Direct revascularisation, Moya-Moya syndrome, Neurofibromatosis, Temporo-cortical anastomosis

Référence

Neurochirurgie. 2018 Mar;64(1):63-67