Medical treatment of mammary desmoid-type fibromatosis: which benefit?

Fiche publication


Date publication

avril 2017

Journal

World journal of surgical oncology

Auteurs

Membres identifiés du Cancéropôle Est :
Pr KURTZ Jean-Emmanuel, Pr MATHELIN Carole


Tous les auteurs :
Scheer L, Lodi M, Molière S, Kurtz JE, Mathelin C

Résumé

Breast fibromatosis is a rare disease characterized by monoclonal fibroblast proliferation. It has no ability to metastasize but has a high local recurrence rate and often infiltrates surrounding tissues. Surgical treatment is the reference, but recently, new targeted therapies have emerged. We report an original case of a patient with breast fibromatosis who received exclusive medical treatment. Our aim was to analyze these treatments based on the clinical and radiological outcome, iatrogenic effects, and pharmacological action.

Mots clés

Breast fibromatosis, Desmoid-type fibromatosis, Extra-abdominal fibromatosis, Sunitinib, Tyrosine-kinase inhibitors, Wnt-beta catenin

Référence

World J Surg Oncol. 2017 Apr;15(1):86