Is Nephron Sparing Surgery Justified in Wilms Tumor With Beckwith-Wiedemann Syndrome or Isolated Hemihypertrophy?
Fiche publication
Date publication
septembre 2016
Journal
Pediatric blood & cancer
Auteurs
Membres identifiés du Cancéropôle Est :
Pr AUBER Frédéric
Tous les auteurs :
Scalabre A, Bergeron C, Brioude F, Dainese L, Cropet C, Coulomb L'hermine A, Pasqualini C, Auber F, Verschuur A, Schleiermacher G, Le Bouc Y, Audry G, Irtan S
Lien Pubmed
Résumé
Patients with Beckwith-Wiedemann syndrome (BWS) or isolated hemihypertrophy (HH) treated for a Wilms tumor (WT) carry an increased risk of developing metachronous lesion. There are no guidelines on precise indications for nephron sparing surgery (NSS) in unilateral WT (UWT). The objective of this retrospective study was to delineate the indications of NSS in patients with BWS/HH treated for WT and to evaluate their outcome.
Mots clés
Beckwith-Wiedemann Syndrome, surgery, Child, Child, Preschool, Female, Humans, Hyperplasia, surgery, Infant, Kidney Neoplasms, surgery, Male, Nephrons, surgery, Retrospective Studies, Wilms Tumor, surgery
Référence
Pediatr Blood Cancer. 2016 09;63(9):1571-7