The French paediatric cohort of Castleman disease: a retrospective report of 23 patients.
Fiche publication
Date publication
avril 2020
Journal
Orphanet journal of rare diseases
Auteurs
Membres identifiés du Cancéropôle Est :
Dr JANNIER Sarah
Tous les auteurs :
Borocco C, Ballot-Schmit C, Ackermann O, Aladjidi N, Delaleu J, Giacobbi-Milet V, Jannier S, Jeziorski E, Maurier F, Perel Y, Piguet C, Oksenhendler E, Koné-Paut I, Galeotti C
Lien Pubmed
Résumé
Castleman disease (CD) is a rare non-malignant lymphoproliferation of undetermined origin. Two major disease phenotypes can be distinguished: unicentric CD (UCD) and multicentric CD (MCD). Diagnosis confirmation is based on histopathological findings in a lymph node. We attempted to survey all cases of paediatric CD identified to date in France to set up a national registry aiming to improve CD early recognition, treatment and follow-up, within the context of a new national reference center (http://www.castleman.fr).
Mots clés
Multicentric, Paediatric Castleman disease, Tocilizumab, Unicentric
Référence
Orphanet J Rare Dis. 2020 Apr 17;15(1):95